Is there any chance that a child with Hirschsprung Disease will pass away?
In someone with Hirschsprung disease, if surgery is not performed soon enough, the colon (the last part of the digestive system and transports digested food and liquid from the small intestine to the rectum), can become very enlarged and rupture. This can be very dangerous and if not treated can cause someone to die. This is why Hirschsprung disease almost always requires surgery. The most common cause of death in young people with Hirschsprung disease is enterocolitis, or infection of the intestines. It important to look out for signs of infection, such as fever, vomiting, less energy, and a large belly. If you are concerned that you or your child are experiencing any of these symptoms contact your physician right away.
Frykman PK, Short SS; "Hirschsprung-associated enterocolitis: prevention and therapy". Semin Pediatr Surg. 2012 Nov;21(4):328-35. doi: 10.1053/j.sempedsurg.2012.07.007.