Glycogen storage disease type III

Treatment

Is there a treatment for glycogen storage disease type 3?

People with glycogen storage disease type 3 (GSD III) cannot turn glycogen into glucose for energy in between meals. Instead of providing energy, the glycogen can build up in the liver and muscles, causing low blood sugar, seizures, lethargy and muscle weakness if left untreated. The treatment for GSDIII is to work with metabolic dieticians and your pediatrician to give your child a high-protein diet and to make sure your child eats every 2-4 hours. A nutritionist or dietician can work with you to develop a healthy diet for your child. Many children with GSD III take extra vitamins such as calcium supplements or a multivitamin. Your medical team may also recommend your child get a feeding tube /or eat a mixture of cornstarch and water to make sure they have enough energy in their body throughout the night. Children with GSD III who follow a strict diet have healthy lives and normal development; however, extra care is needed when they are sick. People with GSD III also need to get routine examinations of their liver and heart.

References
  • http://www.agsdus.org/html/typeigsd.html
  • Dagli A, Sentner CP, Weinstein DA. Glycogen Storage Disease Type III. 2010 Mar 9 [Updated 2012 Sep 6]. In: Pagon RA, Adam MP, Ardinger HH, et al., editors. GeneReviews® [Internet]. Seattle (WA): University of Washington, Seattle; 1993-2016. Available from: http://www.ncbi.nlm.nih.gov/books/NBK26372/
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Is there a cure for glycogen storage disease type 3?

Is there a cure for glycogen storage disease type 3?

Currently there is no cure for glycogen storage disease type 3. However, children who follow a strict diet generally grow healthy and well. Even if people with GSD III follow a strict diet, other health problems can develop later in life such as muscle weakness or heart issues. Therefore, people with GSD III will need to be followed closely by doctors throughout their lifetime.

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