Arrhythmogenic right ventricular cardiomyopathy
What treatments are available for arrhythmogenic right ventricular cardiomyopathy?
Treatment for arrhythmogenic right ventricular cardiomyopathy is more focused on managing symptoms because there is no cure for it. Management is focused on prevention of fainting, cardiac arrest, and sudden death. Additionally, beta blockers are considered first line therapy. Although their efficacy has not been shown in a randomized, prospective clinical trial, beta blockers are recommended. Arrhythmia prevention relies on device insertion and management. Education regarding sudden death risk to affected adults and parents of affected children is an important aspect of management. Physical exercise specifically regular, intense exercise is thought to worsen ARVC and its associated arrhythmias. Therefore, those with fully diagnosed ARVC are usually recommended to reduce or eliminate prolonged exercise and participation in competitive sports. Heart transplantation is considered when ARVC has progressed to right or left ventricular heart failure.
SOURCE: Emory University - Department of Human Genetics in collaboration with ThinkGenetic • https://www.thinkgenetic.com/diseases/arrhythmogenic-right-ventricular-cardiomyopathy-109924/treatment/66395 • DATE UPDATED: 2019-06-18
Accessed March 29, 2019: https://www.ncbi.nlm.nih.gov/books/NBK1131/#arvd.Management