Arrhythmogenic right ventricular cardiomyopathy
What treatments are available for arrhythmogenic right ventricular cardiomyopathy?
Treatment for arrhythmogenic right ventricular cardiomyopathy (ARVC) is focused on reducing the risk of developing symptoms, managing existing health issues, and preventing complications like cardiac arrest and sudden death. Lifestyle modifications such as eating a healthy diet, maintaining a healthy weight, avoiding strenuous physical activity, and quitting smoking may be recommended to reduce current and future heart issues. Prescription medications like beta blockers may be used to reduce blood pressure and decrease the amount of work the heart does on a daily basis. Implanted devices like implantable cardioverter defibrillators (ICD) or pacemakers may be used in individuals with ARVC to control abnormal heart rhythms (arrhythmias), identify any life-threatening arrhythmias, and deliver an electrical shock to 'reset' the heart's rhythm as needed. Heart transplantation may be considered when ARVC has progressed to right and/or biventricular heart failure.
The creation of an individualized monitoring and treatment plan for a person with ARVC is most often designed by a cardiologist and/or electrophysiologist familiar with the progression of the condition. You can seek out a specialist at the Heart Rhythm Society's "Find a Specialist page at https://www.hrsonline.org/find-a-specialist or by asking your doctor for a referral to a heart and vascular institute.
The British Heart Foundation also has an excellent brochure that describes treatments for ARVC called "Inherited heart conditions: Arrhythmogenic right ventricular cardiomyopathy". https://www.cardiomyopathy.org/downloads/information-section/bhf-booklets/arrhythmogenic-right-ventricular-cardiomyopathy.pdf.
SOURCE: Emory University - Department of Human Genetics in collaboration with ThinkGenetic • https://www.thinkgenetic.com/diseases/arrhythmogenic-right-ventricular-cardiomyopathy-109924/treatment/66395 • DATE UPDATED: 2019-11-16
McNally E, MacLeod H, Dellefave-Castillo L. Arrhythmogenic Right Ventricular Cardiomyopathy. 2005 Apr 18 [Updated 2017 May 25]. In: Adam MP, Ardinger HH, Pagon RA, et al., editors. GeneReviews® [Internet]. Seattle (WA): University of Washington, Seattle; 1993-2019. Available from: https://www.ncbi.nlm.nih.gov/books/NBK1131/ Accessed March 29, 2019.
British Heart Foundation "Inherited heart conditions: Arrhythmogenic right ventricular cardiomyopathy". https://www.cardiomyopathy.org/downloads/information-section/bhf-booklets/arrhythmogenic-right-ventricular-cardiomyopathy.pdf Accessed 29MAR2019.
Heart and Vascular Institute, ARVD/C Questions and Answers. https://www.ahajournals.org/doi/10.1161/CIRCULATIONAHA.113.004845 Accessed 11NOV19