Arrhythmogenic right ventricular cardiomyopathy
Tell me about arrhythmogenic right ventricular cardiomyopathy.
Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a genetic heart condition that is characterized by progressive replacement of the heart muscle (myocardium) with an combination of abnormal fat and scar tissue called "fibrofatty tissue". This process increases the chance that a person will have heart rhythm abnormalities such as ventricular tachycardia (a fast, abnormal heart rate). Abnormal heart rhythms can lead to sudden death, particularly in young individuals and athletes. ARVC affects the bottom right side of the heart (the right ventricle) but may affect the bottom left side of the heart (left ventricle) as well. ARVC can affect individuals differently from family to family and from individual to individual. The average age at diagnosis is 31 years, but children as young as 4 years old to as old as 64 years old have been found to have ARVC. If diagnosed early and treated aggressively, people with this condition often do quite well.
SOURCE: Emory University - Department of Human Genetics in collaboration with ThinkGenetic • https://www.thinkgenetic.com/diseases/arrhythmogenic-right-ventricular-cardiomyopathy-109924/overview/66379 • DATE UPDATED: 2019-11-13
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